Près de 1 220 personnes sont atteintes de fibrose kystique au Québec. De ce nombre, un peu plus de 130 sont au Saguenay-Lac-Saint-Jean. C’est notamment le cas de la petite Gabrielle, âgée de vingt-trois mois. “C’est une nouvelle que nous attendions. Gabrielle aura deux ans dans un mois, alors elle n’est pas encore assez âgée pour avoir Trikafta », a déclaré sa mère, Stéphanie Dionne. Dans quatre ans, Gabrielle pourra recevoir le médicament gratuitement, ce qui est un grand soulagement pour sa mère, qui n’a plus à se soucier de devoir payer le traitement de sa fille....

Having just hosted the Commonwealth Games, Birmingham is one of the cities shortlisted to be the next Eurovision venue, but are they up to the challenge? reports Rishi Davda Scott Mills joined Zoe Ball on BBC Radio 2 Breakfast to announce that Birmingham, Glasgow, Leeds, Liverpool, Manchester, Newcastle and Sheffield had been shortlisted as potential host cities. Twenty cities had expressed interest in hosting the 67th Eurovision Song Contest, and those not shortlisted include London and Belfast....

The flood warning follows days of extreme heat warnings and an official drought declaration following the longest nine-month drought since 1976. Forecasters warned that downpours are the wrong kind of rain to deal with drought and are more likely to lead to flooding than water flowing from parched land. The heatwave is forecast to break with a yellow warning for thunderstorms covering almost the whole of the UK on Monday, all of England and Wales on Tuesday and most of southern and eastern England on Wednesday....

Serhiy Haidai, governor of the Luhansk region in eastern Ukraine, said the base was “destroyed by a precision strike” after its location was established “thanks to a Russian journalist”. Ukrainian news website Ukrainska Pravda reported that a Kremlin military correspondent visited the mercenary headquarters on August 8 and posted a photo on Telegram showing a nearby address. The paramilitary group has been linked by Western intelligence to Russian oligarch Yevgeny Prigozhin, who is a close associate of Vladimir Putin....

“Schädigt großen Schaden” – Diskussionsrückblick zur vierten Impfung Stand: 14:59 Uhr| Lesezeit: 2 Minuten Lauterbachs Corona-Regeln werden kritisiert und verwechselt Lauterbach will nicht missverstanden werden: Er habe nie alle drei Monate um eine Auffrischungsimpfung gebeten. Bundeskanzler Scholz springt ein und erklärt, dass niemand für eine solche Dreimonatsfrist sei. Diese Flecken auf dem Corona-Design von Lauterbach sorgen für Kopfschütteln. Die Debatte über eine vierte Coronavirus-Impfung wird nun auch in Deutschland heftig geführt....

The finale opens with a street littered with corpses. Civilians kill each other without mercy or ceremony, turning once peaceful city blocks into veritable war zones. Fleeting guest castings come and go. (Hello, Stephen Ogg!) A young marksman takes out a handful of these murderous pedestrians before William kills him. The Man in Black has plunged the world into chaos and returned to his element. Back at the tower, Hale’s faceless subordinates retrieve and revive her....

Michael Gableman’s firing capped a 14-month run that began when Assembly Speaker Robin Vos hired him to look into the election under pressure from Trump. But as the investigation progressed under bipartisan criticism, Vos’ relationship with both Trump and Gableman soured. Vos initially said he was “extremely confident” in Gableman’s abilities. After his election victory Tuesday, Vos called Gableman “an embarrassment to himself” and the state. Gableman, who has repeated Trump’s lie that the 2020 presidential election was “stolen,” said Vos “never wanted a real investigation....

Workers from Zaporizhzhia facility describe disappearances at hands of Russian soldiers and fear of nuclear holocaust August 15, 2022 at 3:15 pm EDT Young men swim in the Dnieper River on August 15, opposite the Zaporizhzhia nuclear complex, which is under the control of Russian forces. (Heidi Levine for The Washington Post) Placeholder when loading article actions ZAPORIZJIA, Ukraine — There is no warning when an impending fire hits the grounds of Europe’s largest nuclear plant, sending workers scrambling for cover....

Die Polizei bittet um Hinweise Ab heute, 19:24 Uhr online Sattledt. Bereits am 31.07.2022 gegen 02:30 Uhr wurden bei einer Veranstaltung in Sattledt zwei Männer im Alter von 25 und 28 Jahren, beide aus dem Raum Wels-Land, von zwei bisher unbekannten Angreifern geschlagen und verletzt. Nach Angaben der Polizei gelang den Tätern nach der Tat, die sich in der zur Disco umfunktionierten Stockschützenhalle ereignete, die Flucht unentdeckt. Beschreibungen des Täters: – Männlich, ca....

“Well, I thought I had a way through the bulletproof glass, and I didn’t,” the user posted at 9:29 a.m. Thursday on Truth Social, Trump’s social media site. “If you haven’t heard from me, it’s true that I tried to attack the FBI and that will either mean I got kicked off the internet, the FBI got me, or the regular cops were sent in. It is not clear if the user was trying to write more, as the post stops after the “while”....

Mountain guides confirmed that Adèle Milloz, 26, and her climbing partner, 30, fell to their deaths on Friday before 6.15pm on the route to Aiguille du Peigne. The climbers were above 10,000 feet, crossing the Aiguille du Peigne to the Aiguille du Midi. Other climbers saw the two fall and called for help. They then stopped their own ascent due to shock and were pulled off the mountain. Ms Milloz grew up in Tignes, in the Alps, and won gold in individual and team sprint ski mountaineering at the Military World Winter Games in Sochi five years ago....

As noted by The Verge, the update finally went out yesterday, and Durov took to Telegram again to discuss what happened. The CEO says Apple told Telegram it should remove a new feature called Telemoji, which Durov described as “higher-quality animated versions of the standard emoji.” He included a preview of what they would look like in his post — they’re similar to the basic set of emojis Apple uses, but with some really nice animations that could definitely help make messages a little more expressive....

Apple initially said that CSAM detection would be implemented in an update for iOS 15 and iPadOS 15 by the end of 2021, but the company eventually postponed the feature based on “feedback from customers, advocacy groups, researchers and others.” . In September 2021, Apple posted the following update on its child safety page: We previously announced plans for features to help protect children from predators who use communication tools to recruit and exploit them, and to help curb the spread of child sexual abuse material....

Thalbinder Singh Poonian and Shailu Poonian owe the BC Securities and Exchange Commission a total of $19 million for market manipulation that a commission panel found they committed. The total includes $13.5 million in administrative penalties and $5.5 million in “disgorgement of their ill-gotten gains,” according to a BCSC statement. In November, the BC Court of Appeal dismissed an appeal by the couple in which they argued that the master who handled their bankruptcy discharge application had erred in several ways when he decided not to discharge them of the BCSC debt....

“There are other infections — syphilis, for example — that are spread in ways other than sexual transmission,” he said. “Zika is a mosquito-borne disease, but it can also be sexually transmitted. The question for me is more about making sure we’re clear about what’s going on physiologically before you make those kinds of claims.” Some experts argue that labeling monkeypox as an STD could be not only misleading but also potentially harmful to public health....

The UFC Hall of Famer lost the Republican primary by a wide margin on Saturday, garnering just 22.2 percent of the vote. Two-time Republican Lt. Gov. Duke Iona won with 47.5 percent of the vote and will face Democratic Rep. Josh Green in the Nov. 8 general election. Penn announced his intention to run for governor last October with a campaign largely focused on lifting Hawaii’s COVID-19-related restrictions. “I have made many mistakes in my life, but I would never run from a fight or sell out my people,” Penn wrote last October....

British gas owner Centrica and Octopus Energy are understood to be backing a plan that would create a multibillion-pound facility to spread the cost of an emergency funding package over a decade, the Guardian can reveal. Partner suppliers ScottishPower and Eon have presented plans to ministers for the ‘tariff deficit fund’ backed by a government guarantee. Under the proposals, first reported by the Sunday Times, commercial banks would put cash into the Treasury, which suppliers could then draw on to fund measures to freeze customers’ default tariff accounts in the current price cap, £1,971, two years....

Mayer (30 ans) avait annoncé la couleur avant d’entrer dans la compétition. Le défi inédit de combiner deux décathlons en trois semaines, et idéalement l’or mondial et européen, était tentant. Mais ça le fait”il ne prendra aucun risque« Avec la moindre vivacité physique, lui qui a l’habitude de se concentrer sur un seul décathlon par saison et qui a été gêné par un tendon d’Achille jusqu’à peu avant les Mondiaux à Eugene (Etats-Unis)....

17.08.2022, 06:00 Uhr Der jetzige Bundeskanzler Scholz traf als erster Hamburger Bürgermeister mehrfach mit dem Warburg-Bankier Olearius zusammen. Während des Cum-Ex-Skandals hat er sich auch im Finanzausschuss des Bundestags dazu geäußert. Doch er machte widersprüchliche Angaben, wie der „Stern“ berichtet. Im Cum-Ex-Fall hat der aktuelle Bundeskanzler Olaf Solz gegenüber parlamentarischen Ausschüssen widersprüchliche Aussagen zu seinen Treffen mit dem Hamburger Banker Christian Olearius gemacht. Das berichtet der „Stern“ unter Berufung auf das als vertraulich eingestufte Protokoll einer Sitzung des Wirtschaftsausschusses des Bundestags im Juli 2020....

KYIV, Ukraine — Two people were injured and infrastructure badly damaged early Tuesday when a large explosion rocked an ammunition depot in Russian-held Crimea in what the Kremlin called an “act of sabotage.” A senior Ukrainian government official, speaking on condition of anonymity to discuss a sensitive matter, said the blasts were the work of Ukrainian special forces operating deep behind enemy lines – the same forces believed to be responsible for a powerful attack against Russian air base in western Crimea last week marked a shift in Ukraine’s strategic capabilities....